109-2-醫學三-26腎臟內科
下列抗體和疾病之間的致病機轉組合,何者錯誤?
Aanti-proteinase-3 antibodies and granulomatosis with polyangiitis
Banti-hyaluronidase antibodies and poststreptococcal glomerulonephritis
Canti-phospholipase A₂ receptor antibodies and primary membranous glomerulonephritis
Danti-α5 NC1 domain of collagen IV antibodies and Goodpasture syndrome
核心考點
腎臟疾病與致病抗體的對應。Goodpasture 症候群(anti-GBM disease)的標的抗原是第 IV 型膠原 α3 鏈的 NC1 domain(α3(IV)NC1),不是 α5。α5 鏈缺陷與 Alport syndrome 有關。